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Anti-SCYL1BP1SCYL结合蛋白1抗体
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更新日期:2026/9/8 4:13:22
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产品型号:BY-6643R
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相关标签:SCYL1BP1,SCYL结合蛋白1抗体,SCYL1BP1SCYL结合蛋白1抗体
详细内容
本公司经销SCYL1BP1,SCYL结合蛋白1抗体,克隆类型为polyclonal,宿主来源是Rabbit,SCYL1BP1SCYL结合蛋白1抗体可应用于WB、elisa、IP、IF、IHC等实验,欢迎垂询订购!
货号:BY-6643R
英文名称:Anti-SCYL1BP1
中文名称:SCYL结合蛋白1抗体
其他名称:名hNTKL BP1; N terminal kinase like binding protein 1; NTKL binding protein 1; NTKL BP1; NTKLBP 1; NTKLBP1; SCY1 like 1 binding protein 1; SCYL1 binding protein 1; SCYL1 BP1.
抗体来源:Rabbit
克隆类型:polyclonal
蛋白分子量:predicted molecular weight: 45kDa
纯化方法:affinity purified by Protein A
交叉反应:hu, mo, rat, pig, cow, chk, hrs, dog, Rb
产品介绍:Defects in GORAB are the cause of geroderma osteodysplasticum (GO) [MIM:231070]; also known as gerodermia osteodysplastica or Walt Disney dwarfism. GO is a rare autosomal recessive disorder characterized by lax, wrinkled skin, joint laxity and a typical face with a prematurely aged appearance. Skeletal signs include severe osteoporosis leading to frequent fractures, malar and mandibular hypoplasia and a variable degree of growth retardation.Subcellular Location : Cytoplasm. Golgi apparatus.Similarity : Belongs to the GORAB family.
货号:BY-6643R
英文名称:Anti-SCYL1BP1
中文名称:SCYL结合蛋白1抗体
其他名称:名hNTKL BP1; N terminal kinase like binding protein 1; NTKL binding protein 1; NTKL BP1; NTKLBP 1; NTKLBP1; SCY1 like 1 binding protein 1; SCYL1 binding protein 1; SCYL1 BP1.
抗体来源:Rabbit
克隆类型:polyclonal
蛋白分子量:predicted molecular weight: 45kDa
纯化方法:affinity purified by Protein A
交叉反应:hu, mo, rat, pig, cow, chk, hrs, dog, Rb
产品介绍:Defects in GORAB are the cause of geroderma osteodysplasticum (GO) [MIM:231070]; also known as gerodermia osteodysplastica or Walt Disney dwarfism. GO is a rare autosomal recessive disorder characterized by lax, wrinkled skin, joint laxity and a typical face with a prematurely aged appearance. Skeletal signs include severe osteoporosis leading to frequent fractures, malar and mandibular hypoplasia and a variable degree of growth retardation.Subcellular Location : Cytoplasm. Golgi apparatus.Similarity : Belongs to the GORAB family.
SCYL1BP1,SCYL结合蛋白1抗体,SCYL1BP1SCYL结合蛋白1抗体


